Jan 5, 2024 · Following a low-phenylalanine diet can prevent intellectual disability and other complications in people with phenylketonuria. The diet focuses on low protein foods and avoids high protein...

Jul 12, 2023 · A PKU diet typically includes a phenylalanine-free medical formula or shake to meet your daily nutritional needs along with carefully measured amounts of fruits, vegetables, breads, pasta, and cereals to ensure you obtain just the …

Dec 8, 2023 · This article discusses which foods people with PKU should include or avoid in a phenylketonuria diet. It also discusses when to speak with a doctor about a PKU diet.

What is a low phenylalanine diet? A low phenylalanine diet is the main treatment for phenylketonuria (PKU). People with PKU must restrict phenylalanine which is found in protein. However, phenylalanine cannot be removed completely, so it is given in measured exchange amounts each day. What is a protein (PKU) exchange?

Phenylketonuria (PKU) is an autosomal recessive inborn error of phenylalanine metabolism caused by deficiency in the enzyme phenylalanine hydroxylase that converts phenylalanine into tyrosine. In 2017 the first European PKU Guidelines were published.

The diet for PKU consists of a phenylalanine-free medical formula and carefully measured amounts of fruits, vegetables, bread, pasta, and cereals. Many people who follow a low phenylalanine (phe) food pattern eat special low protein breads and pastas.

Apr 24, 2017 · Phenylketonuria, or PKU, is a genetically inherited birth defect that causes an unwanted buildup of the amino acid phenylalanine in the blood, and a strict diet limited in phenylalanine is the main treatment.

Treating PKU Diet. The main treatment for PKU is a low-protein diet and controlled intake of many other foods, such as potatoes and cereals. High protein foods should be completely avoided. These include: meat and fish; eggs and cheese; nuts and seeds; flour-based foods, like bread, pasta, cakes and biscuits; soya, quorn and tofu

The PKU diet regime is a low phenylalanine diet, ie very low in protein containing foods, and when the phenylalanine content of food is known a phe exchange value is allocated, otherwise, protein values are used, which can mean interpreting the label on manufactured foods.

When you have phenylketonuria (PKU), you need to follow a lifelong special diet. Having PKU means your body can’t break down an amino acid called phenylalanine (Phe). Amino acids are building blocks of protein.