Nov 27, 2023 · Michel aplasia or deformity, also known as complete labyrinthine aplasia, is the most severe congenital inner ear malformation, characterized by complete absence of inner ear structures (cochlea, vestibule, semicircular canals, and vestibular and cochlear aqueducts).

CLA, also called Michel anomaly or Michel aplasia, is a rare congenital anomaly of the inner ear, constituting 1% of cochlear bony abnormalities. 2 CLA is defined by complete absence of inner ear structures due to a developmental arrest of the otic placode before the third gestational week. 12 This anomaly was first reported by Michel in the ...

Complete labyrinthine aplasia is an inner ear malformation characterized by the total absence of cochleovestibular structures, accounting for approximately 1% of cases of cochlear malformations [8]. It is also called Michel aplasia because it was first described in 1863 by Eugéne Michel [2].

Michel aplasia, also known as complete labyrinthine aplasia, is a rare congenital inner ear abnormality, accounting for approximately 1% of cochlear bony malformations.

We have discussed here that three year old girl diagnosed Michel aplasia with temporal bone computed tomography (CT) and temporal magnetic resonance imaging (MRI) findings. Keywords: neurosensory, aplasia, otic placode, imaging findings. 1. INTRODUCTION. Congenital inner ear abnormality is the most common cause of neurosensory hearing loss .

Michel aplasia is a rare developmental anomaly refers to the total aplasia of the inner ear.

Jun 11, 2022 · Complete labyrinthine aplasia (CLA) is the absence of the cochlea, vestibule, semicircular canals, vestibular, and cochlear aqueducts and is also known as Michel deformity. There are three radiological subtypes.

Feb 1, 1999 · We report two patients with a total absence of inner ear structures bilaterally, illustrating the characteristic appearance of Michel aplasia and associated skull base anomalies.

Michel aplasia, also known as complete labyrinthine aplasia (CLA), is a congenital abnormality of the inner ear. It is characterized by the bilateral absence of differentiated inner ear structures and results in complete deafness ( anacusis ).

Michel aplasia, also known as complete labyrinthine aplasia (CLA), is a congenital abnormality of the inner ear. It is characterized by the bilateral absence of differentiated inner ear structures and results in complete deafness (anacusis).